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What is the prognosis of Scimitar syndrome?
Does age influence the outcome of surgical treatment of Scimitar syndrome?
What is the prevalence of Scimitar syndrome?
Apr 11, 2022 · Some adults who have scimitar syndrome may live healthy lives without needing surgery. Most adults who have surgery for scimitar syndrome have excellent outcomes with typical life expectancy. Medically Reviewed
Dec 19, 2022 · A successful surgery typically enables long-term survival and healthy life. Surgery for scimitar syndrome can, however, be challenging and difficult, especially for young babies. Complications, such as narrowing of the pulmonary vein (pulmonary vein stenosis) and surgical mortality (death), are possible.
- Corey Whelan
Aug 4, 2022 · Results: 34 patients, including 16 males and 18 females, were enrolled with a median age at diagnosis of 7 months and a follow-up period of 22.5 months. The infantile form of Scimitar syndrome presents more tendency for pulmonary hypertension (PH), pulmonary vein stenosis (PVS), and mortality than the adult form.
Jul 15, 2008 · Scimitar syndrome can be associated with congenital cardiovascular defects (dextrocardia, atrial septal defects, and right pulmonary artery hypoplasia), pulmonary anomalies (hypoplasia, sequestration), and tracheobronchial anomalies. Thus, it can manifest with heart failure and recurrent pneumonia. 1,2. Diagnosis is obtained during childhood ...
When diagnosed in infancy, the syndrome is associated with significant mortality due to severe respiratory insufficiency, cardiac failure, and pulmonary infections. Last update: May 2009 - Expert reviewer(s): Pr Robert ANDERSON
Feb 27, 2024 · What is Scimitar Syndrome? Scimitar Syndrome, also known as hypogenic lung syndrome or pulmonary venolobar syndrome, is a rare congenital abnormality affecting 1 – 3 in 100,000 babies born. It affects more females than males. In this syndrome, the right lung of the fetus is poorly developed and there is abnormal drainage of the lung vein.
What is Scimitar Syndrome? Scimitar Syndrome, also known as hypogenic lung syndrome or pulmonary venolobar syndrome, is a rare congenital abnormality affecting 1 – 3 in 100,000 babies born. It affects more females than males. In this syndrome, the right lung of the fetus is poorly developed and there is abnormal drainage of the lung vein.
