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- This condition can be managed with medical care, and sometimes surgical intervention is needed. Spherocytosis is not curable, but medical attention can help improve the outcome and quality of life and prevent complications.
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May 19, 2022 · Hereditary spherocytosis is a rare inherited disorder that requires lifelong medical care. Healthcare providers can treat the sometimes-serious medical conditions that hereditary spherocytosis causes. They can’t cure the blood disorder, though. It’s not always easy to have a chronic illness or care for someone who does.
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Management depends on the severity of the hemolysis and degree of anemia, but is generally supportive for most patients. Splenectomy is the treatment of choice in patients with severe HS. This is best avoided until at least 6 years of age to reduce the risk of postsplenectomy sepsis.
Glucocorticoids are the initial treatment of choice for canine, feline and human IMHA. They interfere with both the expression and function of macrophage Fc receptors and thereby immediately impair the clearance of antibody-coated erythrocytes by the macrophage system.
Jul 4, 2023 · Hereditary spherocytosis (HS) is the most prevalent cause of hemolytic anemia due to an abnormal red cell membrane and classifies as a type of congenital hemolytic anemia. Oskar Minkowsky first described it in the early 1900s. [1] .
- Edgar A. Zamora, Catherine A. Schaefer
- 2023/07/04
Feb 14, 2024 · What Is the Treatment for Hereditary Spherocytosis? Treatment for this disorder depends on its severity. If you have a mild form of hereditary spherocytosis, your doctor will likely recommend...
Mar 6, 2023 · In most people, splenectomy — or removal of the spleen — can cure symptoms. However, this procedure can increase the risk of serious infections and pose other surgery-related risks.
Oct 24, 2021 · Background. Hereditary spherocytosis (HS), a commonly encountered hereditary hemolytic disease, is mostly inherited in an autosomal dominant manner. The clinical manifestations in patients with HS show obvious heterogeneity.
