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Jun 26, 2023 · Scimitar syndrome is primarily an imaging diagnosis and gives a characteristic abnormal chest X-ray that shows the shadow of the descending pulmonary vein along the right cardiac border, a hypoplastic lung, as well as dextroposition of the heart.
- Josue Diaz-Frias, Jason Widrich
- 2023/06/26
- Types of Scimitar Syndrome
- Symptoms
- Diagnosis
- Treatment
- Prognosis
- Coping
- Summary
- A Word from Verywell
Since symptom severity varies significantly between infants and adults, this condition is classified into infantile and adult forms, as follows: 1. Infantile form: This form is categorized by the early onset of severe symptoms. Babies with the infantile form of scimitar syndrome have a mortality rate of up to 45%. 2. Adult form: This form is usuall...
Scimitar syndrome symptoms range from nonexistent (asymptomatic) to severe in babies. Babies born with serious symptoms or cardiac complications, such as pulmonary hypertension (higher than normal pressure in the pulmonary artery) or pulmonary vein stenosis(narrowing), may be diagnosed in infancy. Symptoms in babies include: 1. Cyanosis(blue or gra...
Diagnosis of scimitar syndrome is usually made through imaging tests, such as a chest X-ray or computed tomography (CT) scan. These tests provide images of the size, shape, and positioning of the pulmonary arteries, lungs, and heart. Babies may be given imaging tests if they have symptoms of scimitar syndrome. They may also be tested if their weigh...
Scimitar syndrome Is repaired surgically in babies. Several surgical techniques can be utilized to reroute the pulmonary vein and correct blood flow. Part of the lung may also be removed as part of treatment. One surgical technique is called a baffling procedure. The surgeon will artificially construct a tunnel within the heart or blood vessels tha...
In symptomatic infants, treatment is required in order to achieve a good prognosis. A successful surgery typically enables long-term survival and healthy life. Surgery for scimitar syndrome can, however, be challenging and difficult, especially for young babies. Complications, such as narrowing of the pulmonary vein (pulmonary vein stenosis) and su...
Your coping ability will be significantly enhanced if you lean on or create a support system. Your baby's healthcare providers can be part of this team. Make sure to ask as many questions as you need and get second opinions as necessary. If you have people in your life, such as a partner, trusted family members, or friends, make them part of your t...
Scimitar syndrome is a type of rare congenital heart defect. Babies born with this condition may be asymptomatic, or have severe symptoms which require surgical correction. Adults with this condition are often asymptomatic. If symptoms such as persistent lung infections occur, surgery may also be necessary to correct scimitar syndrome in this popul...
If you're the parent or caregiver of a baby with scimitar syndrome, you may find yourself in the unwanted position of having to make scary decisions about their care. You may also need to find the balance between taking care of your baby and taking care of yourself. None of this is easy. Try to remember and believe that there is no one and nothing ...
- Corey Whelan
People also ask
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Is scimitar syndrome a congenital malformation?
Scimitar, or pulmonary venolobar, syndrome is a rare but well-known congenital cardiovascular defect that includes a hypoplastic right pulmonary artery and right lung, which leads to displacement of cardiac structures into the right hemithorax, anomalous systemic arterial supply to the right lung, and a characteristically curved anomalous right ...
Jan 24, 2020 · Scimitar syndrome (SS) is a rare congenital heart anomaly consisting of anomalous venous drainage of part or the entire right lung into the upper portion of the inferior vena cava (IVC), right lung hypoplasia, and a variable systemic arterial blood supply to the right lung.
- Vladimiro L. Vida, Alvise Guariento
- 2020
Scimitar syndrome (SS) is a rare congenital heart anomaly consisting of anomalous venous drainage of part or the entire right lung into the upper portion of the inferior vena cava (IVC), right lung hypoplasia, and a variable systemic arterial blood supply to the right lung. 1, 2
- Vladimiro L. Vida, Alvise Guariento
- 10.1016/j.xjtc.2020.01.017
- 2020
- JTCVS Tech. 2020 Mar; 1: 75-80.
Aug 24, 2022 · Infantile Scimitar syndrome needs intense suspicion for early diagnosis and multidisciplinary treatment. Interventional treatment of Scimitar syndrome alleviates pulmonary artery pressure and progression during infancy.
Jul 15, 2008 · Scimitar syndrome can be associated with congenital cardiovascular defects (dextrocardia, atrial septal defects, and right pulmonary artery hypoplasia), pulmonary anomalies (hypoplasia, sequestration), and tracheobronchial anomalies. Thus, it can manifest with heart failure and recurrent pneumonia. 1,2
